Sunct syndrome belongs together with cluster headache and hemicrania continua to the group of trigeminal autonomic cephalalgias and was described as more or less untreatable for a long time. Medical management abortive treatments preventive treatments since the attacks are very short lasting, attack therapy strategies are not useful in sunct suna. Sunct syndrome responding absolutely to steroids in two. Sunct headache is a clinical diagnosis supported by a combination of clinical history, normal physical examination, radiography, and mri. It was first described in 1978 and fully characterized in 1989 1, 2. The therapeutic benefits of many drugs are disappointing. Shortlasting unilateral neuralgiform headache with conjunctival injection and tearing sunct is a rare headache disorder characterized by extremely frequent attacks of unilateral head pain and autonomic activation. It can be distinguished from other closely similar primary headaches because of the usually very brief attack duration 15120 seconds which can.
Sunct syndrome in two patients with prolactinomas and bromocriptineinduced attacks. Doctors suspended treatment with cabergoline and began lamotrigine dosed at 50mg12h. Sunct syndrome secondary to prolactinoma journal of. Significance of atypical presentation of symptomatic sunct. Sunct, like cluster headache, is a primary headache disorder characterized by. Pain syndromes that may mimic sunct headache include cluster headache, temporal arteritis, trigeminal neuralgia involving the first division of the trigeminal nerve, demyelinating disease, primary stabbing headache, hypnic headache, and chronic paroxysmal. J headache pain sunct syndrome treated with gamma knife targeting the trigeminal nerve and sphenopalatine ganglion thomas mathew 0 1 dwarakanath srinivas 0 1 sushanth aroor 0 1 chandrajit prasad 0 1 sampath somanna 0 1 raghunandan nadig 0 1 g. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct or cranial autonomic features suna a prospective clinical study of sunct and suna. Wed like to understand how you use our websites in order to improve them. Sunct and suna are rare primary headache disorders that are distinct. Article information, pdf download for sunct syndrome with. Sunct syndrome risks, symptoms and leading causes treato. Sunct syndrome, sunct headache ouchuk cluster headache. Secondary sunct syndrome caused by dorsolateral medullary infarction di jin, yajun lian and haifeng zhang abstract shortlasting unilateral neuralgiform headaches with conjunctival injection and tearing sunct is a rare headache syndrome which belongs to trigeminal autonomic cephalalgias.
To date, anticonvulsants seem to be the drugs of choice with preference for lamotrigine 7,1012, topiramate 7,16, and gabapentin 7,1719. For language access assistance, contact the ncats public information officer. A version of this article was copy edited by despayre, a member of the guild of copy editors, on march 4, 2012. Sustained response to botulinum toxin in sunct syndrome. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. Pathogenesis, surgical treatment, and cure for sunct syndrome isao kitahara1, ataru fukuda1, yoshiki imamura2, masako ikawa3, tomoki yokochi4background. Sunct syndrome shortlasting unilateral neuralgiform. Methylprednisolone therapy for shortterm prevention of sunct syndrome. Tmj derangement and sunct syndrome comorbidity page 2. Sunct syndrome successfully treated with the combination of. Frontiers comorbid sunct syndrome and opalski syndrome. Sunct syndrome has been previously described in association with lms.
According to the international classification of headache disorders ichdiii, they include longlasting headaches such as cluster. Also some minor modifications of the hitherto known clinical symptomatology of sunct syndrome have been observed. Shortlasting unilateral neuralgiform headache with. At around 30, this male patient had developed cycles of unilateral, ocularperiorbital, mostly lowgrade pain sjaastad et al 1978. Symptoms include excruciating burning, stabbing, or electrical headaches mainly near the eye. Sunct syndrome is listed as a rare disease by the office of rare diseases ord of the national institutes of health nih. Vascular malformation of the cerebellopontine angle. Synopsis sunct is a headache syndrome characterized by shortlasting usually 15120 sec, unilateral head pain paroxysms localized in the periocular area, accompanied. The attacks are strictly unilateral, generally with the pain persistently confined to the ocularperiocular area. Moreover, this case report may stimulate the interest of headache experts on a lumpersplitter problem, with our patient being an example that could drive attention to several other cases observed in clinical practice. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct are characterized by attacks of moderate to severe. Sunct syndrome is an acronym for shortlasting unilateral neuralgiform headache with conjunctival injection and tearing, it is a type of painful headache that is characterized as one sided and usually around the eye area. The headache seemed rather stable at this level until he, at 58, was struck by the end of a fishing rod in the lower, medial, supraorbital area on the symptomatic side. The patient reported stabbing pain in the orbital zone and in the left upper maxillary region, of great intensity, brief duration, and a frequency of 20100 attacks a day.
Endocrinologists treating patients with prolactinoma need to be. The intense pain is typically localized at the distribution of the first division. Although rarely seen, clinical status may be a feature of the sunct syndrome. Secondary sunct syndrome caused by dorsolateral medullary. Sunct syndrome shortlasting unilateral neuralgiform headache attacks with. Shortlasting unilateral neuralgiform headaches with conjunctival injection and tearing sunct is a rare headache syndrome which belongs to trigeminal autonomic cephalalgias. Shortlasting unilateral neuralgiform headache attacks with. Subsequently, 11 sunct and 4 suna patients reported a favourable outcome during administration of iv lidocaine at the dose of 1. Administration of dopamine agonists led to complete resolution of the. Sunct syndrome, sunct headache, shortlasting unilateral neuralgiform headache attacks with conjunctival injection or tearing, suna headache, shortlasting unilateral neuralgiform headache attacks with cranial autonomic symptoms.
Short lasting unilateral neuralgiform headache attacks with conjuntival injection and tearing sunct also manifests itself as a onesided headache and is associated with the autonomic symptoms as described in cluster headache ch. Sunct syndrome successfully treated with topiramate. The patient reported stabbing pain in the orbital zone and in the left upper maxillary region, of great intensity, brief duration, and a. Report of a case and treatment update cosme gayescoda 1, gemma mayorsubirana 2, octavi campsfont 3, leonardo beriniaytes 4 1 md, dds, ms, phd. Appropriate supplementary examinations ruled out an intracranial lesion in all four patients. Sunct shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearingis a rare form of headache that is most common in men after age 50. Shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearing sunct syndrome is a rare headache, described by our group in 1989. Sunct syndrome treated with gamma knife targeting the. Though the majority of sunct syndrome is idiopathic, more and more cases of secondary sunct syndrome have been reported recently. Sunct syndrome s hort lasting u nilateral n euralgiform headache attacks with c onjuntival injection and t earing sunct also manifests itself as a onesided headache and is associated with the autonomic symptoms as described in cluster headache ch. We report a case of sunct syndrome secondary to a prolactinoma.
Lets not forget that there are 12 pairs of cranial nerves that feed in the pharengeal arches in some measure. When the illness began, the pain was intermittent and short. Consider sunctsuna ouchuk cluster headache charity. Sunct suna short lasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct also manifests itself as a onesided headache and is associated with the cranial autonomic symptoms as described in cluster headache ch. If you previously purchased this article, log in to readcube. Pathogenesis, surgical treatment, and cure for sunct. Mar 27, 2019 sunct shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearingis a rare form of headache that is most common in men after age 50.
Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct syndrome is a rare form of primary headache disorder, although secondary causes, particularly posterior fossa abnormalities, are well known. Headache induced by dopamine agonists prescribed for. They are the first female sunct cases reported of a total of 16 cases hitherto seen by us, reported to us, or published. We describe one case of sunct syndrome secondary to consumption of ergoline dopamine agonist in a patient with. The first sunct patient was observed in 1977, at 62 years of age. Sunct syndrome may be associated with pituitary prolactinoma and may be induced by treatment of prolactinoma with dopamine agonists. Two female patients suffering from sunct syndrome are presented. Sunct suna syndromes diagnosis, prognosis, and treatment sunct suna syndrome is commonly incorrectly diagnosed as trigeminal neuralgia. Pdf shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is characterized by.
Chairman and professor of oral and maxillofacial surgery. Idiopathic sunct syndrome is clinically indistinguishable from sunct syndrome caused by a structural lesion. Tmj derangement and sunct syndrome comorbidity ziconotide combination intrathecal therapy case report of signs and symptoms of internal derangement of the temporomandibular joint tmj comorbid with shortlasting unilateral neuralgiform headache attacks from conjunctival injection and tearing sunct syndrome. Sunct is a syndrome of shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing. Tmj derangement and sunct syndrome comorbidity case report of signs and symptoms of internal derangement of the temporomandibular joint tmj comorbid with shortlasting unilateral neuralgiform headache attacks from conjunctival injection and tearing sunct syndrome. If you have problems viewing pdf files, download the latest version of adobe reader. We are reporting the first case of a clustersunct syndrome. Due to the conspicuous ictal, ocular phenomena, ie, conjunctival injection and tearing, our studies started out with ocular parameters. Sunctshortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearingis a rare form of headache that is most common in men after age 50. Suggested criteria for its diagnosis include attacks of unilateral, moderately severe orbital or temporal stabbing or throbbing pain lasting 5240 s, with an attack frequency of 3200 per day and pain is.
Administration of dopamine agonists led to complete resolution of the sunct attacks. Sunct syndrome successfully treated with the combination. Shortlasting unilateral neuralgiform headache attacks. Pdf sunct syndrome shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing is a primary. If you have questions, please direct them to our talk page. Sunct shortlasting unilateral neuralgiform headache attack with. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a rare but disabling primary headache disorder characterized by brief, severe, ipsilateral, orbitotemporal pain with autonomic features such as conjunctival injection, tearing, and rhinorrhea. This page includes the following topics and synonyms.
Pain attacks may be severe, frequent, and prolonged. Results for sunct syndrome 1 8 of 8 sorted by relevance date click export csv or ris to download the entire page or use the checkboxes to select a subset of records to download export csv export ris 10 per page 50 per page 100 per page 250 per page. Nov 20, 2008 sunct is a syndrome of shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing. This overview presents our early studies of sunct pathogenesis. Sunct syndrome in association with persistent horner syndrome in a chinese patient. Phenotypic and treatment outcome data on sunct and. Pathogenesis, surgical treatment, and cure for sunct syndrome. Sunct syndrome associated with compression of trigeminal nerve. Sunct syndrome or first division trigeminal neuralgia associated. Shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearing sunct is a rare condition grouped in the category of trigeminal autonomic cephalalgia. Methylprednisolone therapy for shortterm prevention of. Sunct emerges as a fairly clearcut, clinical syndrome. Methylprednisolone therapy for shortterm prevention of sunct.
The syndrome is characterized by very frequent, unilateral attacks of pain in the ocular and periocular region accompanied by ipsilateral conjunctival injection and lacrimation. To obtain mechanistic insights into the pathogenesis of sunct syndrome, more than. We are presenting now two cases absolutely responders to steroid therapy, one of them a sunct like secondary to a prolactinoma and the other primary. The disorder is marked by bursts of moderate to severe burning, piercing, or throbbing pain, usually on one side of the head and around the eye or temple. Apr 01, 2015 the present report describes a sunct syndrome in a 64yearold male who had been diagnosed with trigeminal neuralgia several years ago. Paroxysmal hemicrania often the result of cervical pressure sunct syndrome, sjaastad syndrome, ion, on, gpn, etc. Medical management abortive treatments preventive treatments since the attacks are very short lasting, attack therapy strategies are not useful in.
Shortlasting unilateral neuralgiform headache with conjunctival injection and tearing sunct syndrome is an unusual cause of headache, mainly described in older adults, and is rare in children. In this study, we present a case of symptomatic sunct syndrome caused by. Rafael benoliel, yair sharav, in orofacial pain and headache, 2008. Neuroimaging should be considered in all tac or taclike disorders, especially when atypical signs or symptoms are present. Indeed an observation period of more than 5 years speaks against a symptomatic etiology of sunct in these cases. This case demonstrates the effectiveness of resection as definitive treatment for sunct syndrome associ ated with. Shortlasting unilateral neuralgiformheadache attacks with conjunctival injection and tearing sunct are characterized by attacks of moderate to severe. Trauma, arteriovenous malformations and pituitary adenomas may have a causative role. Kopfschmerz, trigeminoautonom, clusterkopfschmerz, sunctsyndrom, paroxysmale hemicranie. Visit our project page if youre interested in joining. Sunct syndrome responding absolutely to steroids in two cases. This means that sunct syndrome, or a subtype of sunct syndrome, affects less than 200,000 people in the us population.
Opalski syndrome is a rare variation of lateral medullary syndrome lms accompanied by ipsilateral hemiparesis. Shortlasting unilateral neuralgiform headaches with conjunctival injection and tearing sunct is a rare headache syndrome which belongs to the trigeminal autonomic cephalalgias. Sunct headache genetic and rare diseases information center. Brain mri is generally recommended for work up to rule out structural lesions responsible for the pain syndrome. Dear editor, it is well known that trigeminal autonomic cephalalgias tacs represent a group of primary headaches characterized by episodes of unilateral, unbearable, stabbing pain associated with a constellation of ipsilateral cranial autonomic features. Indeed, an observation period of more than 5 years speaks against a symptomatic etiology of sunct in these cases. The present report describes a sunct syndrome in a 64yearold male who had been diagnosed with trigeminal neuralgia several years ago. Nevada headache institute 8285 west arby avenue, suite 320 phone. In this study, we present a case of symptomatic sunct syndrome caused by acute. Beim sunctsyndrom shortlasting unilateral neuralgiform headache with conjunctival.